Polyostotic fibrous dysplasia of the craniofacial bones: a case report

Derry Haryono; Menik Priaminiarti; Aloysius Putut Wijanarko; Inka Saraswati; Nissia Ananda

doi:10.32793/jrdi.v10i1.1419

Authors

Derry Haryono Resident in Dentomaxillofacial Radiology Department, Faculty of Dentistry, Universitas Indonesia, Jakarta, Indonesia, 10430, Indonesia
Menik Priaminiarti Universitas Indonesia, Indonesia http://orcid.org/0000-0001-6574-6928
Aloysius Putut Wijanarko Universitas Indonesia, Indonesia http://orcid.org/0009-0005-4580-156X
Inka Saraswati Universitas Indonesia, Indonesia http://orcid.org/0000-0002-9773-0223
Nissia Ananda Rumah Sakit Universitas Indonesia, Indonesia http://orcid.org/0000-0003-2445-1618

DOI:

https://doi.org/10.32793/jrdi.v10i1.1419

Keywords:

fibrous dysplasia, panoramic radiograph, CT-scan

Abstract

Objectives: This case report is aimed to show the radiographic features of fibrous dysplasia, a rare benign condition of abnormal bone growth that progresses slowly and is marked by uneven bone trabeculae interspersed with excessive proliferation of cellular fibrous connective tissue.

Case Report: An 18-year-old female patient with a chief complaint of swelling on the right upper cheek was referred to the Oral and Maxillofacial Department of Universitas Indonesia Hospital. The patient is then referred to the Radiology Department to undergo a panoramic and CT scan examination. On panoramic and CT examination, signs typical of polyostotic fibrous dysplasia were found, namely “ground glass appearance” with ill-defined borders, which extended unilaterally and extended from the maxilla and mandible to the frontal bone.

Conclusion: Polyostotic fibrous dysplasia can be identified on panoramic radiographs, a reliable and widely available diagnostic tool. Computed tomography (CT) is an advanced imaging modality for further evaluation of the lesion extension and tissue involvement. Management requires careful consideration of multiple clinical and radiographic factors.

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